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28-8-第八节 混合性结缔组织病
混合性结缔组织病(mixed connective tissue disease, MCTD)是指多种免疫性疾病同时共存,如SLE、多发性肌炎、系统性硬化及高滴度抗含有 U1 RNP颗粒的RNP抗体。 1 O: _* I6 ]: v! t2 ^- }! L
* W9 f/ u) t7 o4 a' U 混合性结缔组织病可表现关节炎、手肿胀、雷诺现象、食管运动异常、肌炎、白细胞减少及贫血、发热、淋巴结肿大、高球蛋白血症。这些表现提示为SLE、多发性肌炎及系统性硬化。这种多重疾病的发生并不完全清楚,大多数学者认为混合性结缔组织病不是一种特殊的疾病。 7 I3 [; W- l& |1 |
( 陈杰 崔全才 )8 n F+ S1 ?6 z. l) k5 U! a
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